Dental prosthetic rehabilitation of Papillon-Lefèvre syndrome: a case report

  • Shweta M. Patil Department of Prosthodontics, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India.
  • Suryakant B. Metkari Department of Oral Pathology and Microbiology, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India.
  • Shilpa Shetty Department of Conservative Dentistry, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India.
  • Savita Thackannwar Department of Oral Pathology and Microbiology, Tatyasaheb Kore Dental College and Research Center, Kolhapur, Maharashtra, India.
  • Sachin C. Sarode | drsachinsarode@gmail.com Department of Oral Pathology and Microbiology, Dr. D.Y. Patil Dental College and Hospital, Dr. D.Y. Patil Vidyapeeth, Pimpri, Pune, India. http://orcid.org/0000-0003-1856-0957
  • Gargi S. Sarode Department of Oral Pathology and Microbiology, Dr. D.Y. Patil Dental College and Hospital, Dr. D.Y. Patil Vidyapeeth, Pimpri, Pune, India.
  • Namrata Sengupta Department of Oral Pathology and Microbiology, Dr. D.Y. Patil Dental College and Hospital, Dr. D.Y. Patil Vidyapeeth, Pimpri, Pune, India.
  • Shankargouda Patil Department of Maxillofacial Surgery and Diagnostic Sciences, Division of Oral Pathology, College of Dentistry, Jazan University, Jazan, Saudi Arabia.

Abstract

Papillon-Lefèvre syndrome (PLS) is a rare disorder characterized by palmar plantar hyperkeratosis and rapidly progressive periodontitis with loss of deciduous and permanent dentition at an early age. It is reported to occur in 1 to 4 individuals per million people. This case report presents highlighting features of the rare PLS in a 17-year old male who complained of discomfort while mastication and it was accompanied with symmetrical, sharply demarcated erythematous plaques involving the skin of the palms and soles, which extended to the finger joints, elbows, and knees. Along with the rough and dry skin, hyperhidrosis of lesion with a foul odor and transverse grooving of nails were noted. The past dental history revealed normal eruption of deciduous teeth followed by pre-mature mobility and shedding in 4-6 months. Permanent teeth also showed normal eruption and early shedding in the next 4-5 years. Complete edentulous maxillary and mandibular arches led to a decrease in alveolar bone and facial heights. There was no similar disorder in the patient’s family but family history revealed the consanguineous marriage of the patient’s parents.

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Published
2020-09-21
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Section
Case Reports
Keywords:
Palmar planter hyperkeratosis, Papillon-Lefèvre syndrome, periodontitis, complete denture.
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How to Cite
Patil, S. M., Metkari, S. B., Shetty, S., Thackannwar, S., Sarode, S. C., Sarode, G. S., Sengupta, N., & Patil, S. (2020). Dental prosthetic rehabilitation of Papillon-Lefèvre syndrome: a case report. Clinics and Practice, 10(3). https://doi.org/10.4081/cp.2020.1285

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